Leiomyosarcomas of Great Vessels

Eszter SZÉKELY1, Janina KULKA1, Imre MIKLÓS2, Péter KALISZKY2

12nd Department of Pathology, Semmelweis University, Budapest, Hungary
21st Department of Surgery, Semmelweis University, Budapest, Hungary


Sarcomas of the great vessels are rare. Altogether 400 such cases have been described in the aorta, the pulmonary artery, and inferior vena cava. The clinical symptoms are generally related to embolic phenomena, aneurysm formation, and widespread metastases, especially to bones. With improved diagnostic modalities more cases are diagnosed and treated surgically. Resection of the tumor may prolong the patient’s life. In this paper authors present two cases of such rare sarcomas. In our first case a tumor has developed in the thoracic aorta with symptoms of imminent aortic dissection. The tumorous nature of the lesion was revealed only histologically, since neither the operation, nor macroscopic picture gave any clue to its tumorous nature. The second case was a male patient with a huge retroperitoneal tumor arising from the inferior vena cava, which was clinically suspected to be a carcinomaarising in the adrenal gland. Pathology & Oncology Research, Vol 6, Nr 3, 233-236, 2000

Key words: leiomyosarcoma; thoracic aorta; aortic dissection; inferior vena cava; retroperitoneal tumor

Received: Dec 22, 1999; accepted: Jul 20, 2000
Correspondence: Eszter SZÉKELY, 2nd Department of Pathology, Semmelweis University, Üllôi út 93 Budapest H-1091, Hungary; Tel: (36-1) 215-0185, Fax: (36-1) 215-6921; E-mail:

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