PATHOLOGY & ONCOLOGY RESEARCHVol. 10 No. 4, 2004

 Report

Desmoplastic Fibroma-Like Tumor of Maxillofacial Region Associated with Tuberous Sclerosis

Roberto VARGAS GONZALEZ1, Walter SAN MARTIN-BRIEKE2, Claudia GIL-ORDUNA3, Fabiola LARA-HERNANDEZ1

1Department of Pathology, Hospital Para el Nino Poblano, Escuela de Medicina Universidad Popular Autónoma del Estado de Puebla, Puebla, Mexico
2Department of Maxillofacial Surgery, Hospital Para el Nino Poblano, Puebla, Mexico
3Department of Estomatology, Hospital Para el Nino Poblano, and Facultad de Estomatologia B.U.A.P., Puebla, Mexico

 

Desmoplastic fibroma is a rare primary tumor of bone that histologically and biologically mimics the extra-abdominal desmoid tumor of soft tissue. It usually presents in patients during the first three decades of life and often involves the mandible or long bones of the skeleton. Its clinical behavior is characterized by a locally aggressive, infiltrating, and destructing course, often with invasion of surrounding tissues but without metastasis. We present herein the clinicopathological features of a desmoplastic fibroma-like tumor involving the left maxillofacial region in a 14-year-old Hispanic boy with tuberous sclerosis. Pathology & Oncology Research, Vol 10, Nr 4, 237-239, 2004

Key words: desmoplastic fibroma; desmoid tumor; bone tumor; tuberous sclerosis


Received: Aug 27, 2004; accepted: Sep 18, 2004
Correspondence: Roberto VARGAS GONZALEZ, Department of Pathology, Hospital Para el Nino Poblano, Escuela de Medicina Universidad Popular Autónoma del Estado de Puebla, Km 1.5 Carretera Federal Puebla-Atlixco Puebla 72190, Mexico, Fax: 52 (222) 2-45-51-97; E-mail: soncoy@msn.com

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